Correctable cause of dilated cardiomyopathy in an infant with heart failure: ALCAPA syndrome

dc.contributor.authorGüvenç, Osman
dc.contributor.authorSaygı, Murat
dc.contributor.authorÖztürk, Erkut
dc.contributor.authorGüzeltaş, Alper
dc.date.accessioned2020-06-15T06:04:05Z
dc.date.available2020-06-15T06:04:05Z
dc.date.issued2015-08-19
dc.description.abstractAnomalous origin of the left coronary artery arising from pulmonary artery ALCAPA syndrome is a rare congenital heart disease seen in children. If untreated, it may lead to congestive heart failure, dilated cardiomyopathy (DCM), ischemic and arrhythmic complications may lead to patient’s death. ALCAPA is diagnosed with echocardiography; in the patients of suspected diagnosis, computerized tomography, magnetic resonance imaging and cardiac catheterization are used for further testing. Surgically correctable ALCAPA syndrome must be considered as etiology of DCM in children. In this report, we presented the case of an infant that was referred to our center with the diagnosis of DCM, who was echocardiographically diagnosed with ALCAPA syndrome and successfully treated with surgery, as well as a review of recent literature.en_US
dc.description.abstractSol koroner arterin pulmoner arterden çıkış anomalisi olarak tanımlanan ALCAPA sendromu, çocuklarda nadir görülen bir konjenital kalp hastalığıdır. Tedavi edilmediği zaman konjestif kalp yetmezliği, dilate kardiyomiyopati (DKM), iskemik ve aritmik komplikasyonlarla hasta kaybedilebilir. Tanı ekokardiyografi bulgularıyla koyulur, tanıdan şüphelenilen olgularda bilgisayarlı tomografi, manyetik rezonans görüntüleme ve kalp kateterizasyonu gibi ileri tetkiklerden faydalanılabilir. Çocukluk çağında DKM tanısı alan hastalarda etiyolojide, cerrahi olarak düzeltme şansı olan ALCAPA sendromu mutlaka düşünülmelidir. Bu yazıda, merkezimize DKM tanısıyla sevk edilen, ekokardiyografi ile ALCAPA sendromu tanısı konulup, başarılı cerrahi tamir yapılan hasta olgu sunumu yapıldı ve son literatür gözden geçirildi.tr_TR
dc.identifier.citationGüvenç, O. vd. (2017). "Correctable cause of dilated cardiomyopathy in an ınfant with heart failure: ALCAPA syndrome". Güncel Pediatri, 15(1), 47-50.tr_TR
dc.identifier.endpage50tr_TR
dc.identifier.issn1304-9054
dc.identifier.issn1308-6308
dc.identifier.issue1tr_TR
dc.identifier.startpage47tr_TR
dc.identifier.urihttps://dergipark.org.tr/tr/download/article-file/902834
dc.identifier.urihttp://hdl.handle.net/11452/11194
dc.identifier.volume15tr_TR
dc.language.isoenen
dc.publisherUludağ Üniversitesitr_TR
dc.relation.journalGüncel Pediatri / The Journal of Current Pediatricstr_TR
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergitr_TR
dc.rightsinfo:eu-repo/semantics/openAccessen_US
dc.subjectALCAPA syndromeen_US
dc.subjectDilated cardiomyopathyen_US
dc.subjectEchocardiographyen_US
dc.subjectALCAPA sendromutr_TR
dc.subjectDilate kardiyomiyopatitr_TR
dc.subjectEkokardiyografitr_TR
dc.titleCorrectable cause of dilated cardiomyopathy in an infant with heart failure: ALCAPA syndromeen_US
dc.title.alternativeSüt çocuğunda kalp yetersizliği ile başvuran dilate kardiyomiyopatinin düzeltilebilir bir nedeni: ALCAPA sendromutr_TR
dc.typeArticleen_US

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