An orbital Langerhan's histiocytosis case of the childhood

Abstract

Langerhan's cell histiocytosis (LCH) is characterised by the local and diffuse infiltration of monocytes which originated from the promonocytes of the bone marrow. Central nervous system involvement occurs in Hand-Schuller-Christian disease and Letterer-Siwe syndrome. LCH of the orbita is reported to be rare in childhood. A one-;year old boy who had pure bone involvement is presented here and the diagnostic and therapeutic approaches are discussed in the light of the literature.