Publication:
Osteochondritis dissecans in a patient with hyperimmunoglobulin E syndrome

dc.contributor.authorSanal, Özden
dc.contributor.authorTezcan, İlhan
dc.contributor.authorErsoy, Figen
dc.contributor.buuauthorKılıç, Sara Şebnem
dc.contributor.departmentTıp Fakültesi
dc.contributor.departmentPediatri Bölümü
dc.contributor.scopusid34975059200
dc.date.accessioned2022-01-21T07:42:25Z
dc.date.available2022-01-21T07:42:25Z
dc.date.issued2002
dc.description.abstractHyperimmunoglobulin E syndrome (hyper-IgE) is a rare immunodeficiency disease associated with recurrent pyogenic infections, chronic eczematoid dermatitis and osteopenia. We present here a 13-year-old girl with hyperimmunoglobulin E syndrome, who developed osteochondritis dissecans (OCD) of the lateral femoral condyle, which is rare. Osteopenia, which is frequently associated with hyper IgE, may predispose the patient to the development of OCD.
dc.identifier.citationKılıç, S. S. vd. (2002). "Osteochondritis dissecans in a patient with hyperimmunoglobulin E syndrome". Turkish Journal of Pediatrics, 44(4), 357-359.
dc.identifier.endpage359
dc.identifier.issn0041-4301
dc.identifier.issue4
dc.identifier.pubmed12458817
dc.identifier.scopus2-s2.0-0036807296
dc.identifier.startpage357
dc.identifier.urihttp://hdl.handle.net/11452/24208
dc.identifier.volume44
dc.identifier.wos000179136500018
dc.indexed.wosSCIE
dc.language.isoen
dc.publisherTürkiye Milli Pediatri Derneği
dc.relation.collaborationYurt içi
dc.relation.journalTurkish Journal of Pediatrics
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi
dc.rightsinfo:eu-repo/semantics/openAccess
dc.subjectBone abnormalities
dc.subjectHyperimmunoglobulin E syndrome
dc.subjectOsteochondritis dissecans
dc.subjectOsteopenia
dc.subject.emtreeAdolescent
dc.subject.emtreeArticle
dc.subject.emtreeDermatitis
dc.subject.emtreeCase report
dc.subject.emtreeDisease predisposition
dc.subject.emtreeEczema
dc.subject.emtreeFemale
dc.subject.emtreeFemur condyle
dc.subject.emtreeHuman
dc.subject.emtreeHyperimmunoglobulinemia E
dc.subject.emtreeImmune deficiency
dc.subject.emtreeOsteochondritis dissecans
dc.subject.emtreeOsteopenia
dc.subject.emtreeRecurrent infection
dc.subject.meshAdolescent
dc.subject.meshFemale
dc.subject.meshHumans
dc.subject.meshJob's syndrome
dc.subject.meshKnee joint
dc.subject.meshOsteochondritis dissecans
dc.subject.scopusJob Syndrome; Mucocutaneous Candidiasis; Gain of Function Mutation
dc.subject.wosPediatrics
dc.titleOsteochondritis dissecans in a patient with hyperimmunoglobulin E syndrome
dc.typeArticle
dc.wos.quartileQ4
dspace.entity.typePublication
local.contributor.departmentTıp Fakültesi/Pediatri Bölümü
local.indexed.atScopus
local.indexed.atWOS

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