Osler hastalığında Abdominal US Bulguları (Olgu Sunumu)
Date
1992
Authors
Journal Title
Journal ISSN
Volume Title
Publisher
Uludağ Üniversitesi
Abstract
Herediter hemorajik telenjiektazi (HHT) veya Osler-Weber-Rendu Hastalığı tüm organları tutabilen otozomal dominant bir hastalıktır. Sistemik fibrovasküler displaziye neden olan hastalıkta vasküler lezyonlar telanjiektazi, arteriovenöz malformasyonlar ve anevrizma klasik üçlüsü şeklinde görülür. Bu çalışmada, karaciğer tutulumu olan bir Osler hastalığı olgusunun US bulguları sunulmuş ve ilgili literatür gözden geçirilmiştir.
Abdominal US findings in Osler's Disease Hereditary hemorrhagic telangiectasia (HHT) or Osler-Weber-Rendu disease is an autosomal dominant disorder, that causes systemic fibromuscular dysplasia, vascular lesions consist of the classical triad of telangiectasias, arteriovenous malformations and aneurysms. In this study, the sonographic findings in a case of Osler's disease with liver involvement were presented and related literature was reviewed.
Abdominal US findings in Osler's Disease Hereditary hemorrhagic telangiectasia (HHT) or Osler-Weber-Rendu disease is an autosomal dominant disorder, that causes systemic fibromuscular dysplasia, vascular lesions consist of the classical triad of telangiectasias, arteriovenous malformations and aneurysms. In this study, the sonographic findings in a case of Osler's disease with liver involvement were presented and related literature was reviewed.
Description
Keywords
Osler hastalığı, Abdominal US Bulguları, Olgu Sunumu, Herediter, Hemorajik, Otozomal dominant, Karaciğer
Citation
Parlak, M. vd. (1992). ''Osler hastalığında Abdominal US Bulguları (Olgu Sunumu)''. Uludağ Üniversitesi Tıp Fakültesi Dergisi, 19(1), 121-124.