Familyal periodik paraliziler (8 olgunun analizi)
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Date
1992
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Publisher
Uludağ Üniversitesi
Abstract
Familyal periyodik paralizi (FPP), birkaç saatten, birkaç güne kadar süren flask parezi atakları ile karakterize nadir bir kas hastalığıdır. Ataklar anında serum K + değerlerine göre hipokalemik, normokalemik ve hiperkalemik FPP tanımlanmıştır. Hastalık patogenezi bilinmemekle birlikte kas hücre membranında sodyum potasyum iyon transport mekanizmasında tutulum olabilir. Bu çalışmada 1973-1991 yılları arasında 8 FPP'li hasta değerlendirildi. Bu hastaların 7'si hipokalemik,1'i normokalemik idi. Kas biyopsisinde, 2 hastada tipik vakuoller görüldü.
Familial periodic paralysis (FPP) is a rare muscle disease characterised by attacks of flaccid paresis lasting from a few hours to several days. FPPs have been defined as hypokalemic, hypokalemic and hyperkalemic according to serum K+ levels during attacks. The pathogenesis of the disorder is unknown but may involve sodium-potassium ion transport mechanism across the muscle cell membrane. In this study we have evaluated 8 patients with FPP between 1973 and 1991. One of them was normokalemic and seven were hypokalemic. The muscle biopsy showed typical vacuoles in 2 patients.
Familial periodic paralysis (FPP) is a rare muscle disease characterised by attacks of flaccid paresis lasting from a few hours to several days. FPPs have been defined as hypokalemic, hypokalemic and hyperkalemic according to serum K+ levels during attacks. The pathogenesis of the disorder is unknown but may involve sodium-potassium ion transport mechanism across the muscle cell membrane. In this study we have evaluated 8 patients with FPP between 1973 and 1991. One of them was normokalemic and seven were hypokalemic. The muscle biopsy showed typical vacuoles in 2 patients.
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Keywords
Familyal periodik paraliziler, Paraliziler, Kas hastalıkları, Muscular diseases
Citation
Turan, Ö. F. vd. (1992). ''Familyal periodik paraliziler (8 olgunun analizi) ''. Uludağ Üniversitesi Tıp Fakültesi Dergisi, 19(2), 241-247.