Melkersson-Rosenthal sendromu: Bir olgu sunumu
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Date
2007
Authors
Melek, Hamide
Köken, Raşit
Bükülmez, Ayşegül
Şen, Tolga Altuğ
Demir, Tevfik
Bahçeli, Elvan
Journal Title
Journal ISSN
Volume Title
Publisher
Uludağ Üniversitesi
Abstract
Melkersson Rosenthal sendromu tekrarlayan periferik fasiyal paralizi, orofasiyal ödem ve fissürlü dil triadı ile karakterize nöro-mukokütan granülomatöz bir hastalıktır. Çocukluk çağında nadir görülen bu sendrom hayatın 2. ve 3. dekadında daha sık görülür. Klasik triadın görülmesi nadirdir ve genellikle monosemptomatik veya oligo semtomatik tutulum izlenir. Bulgulardan bir veya ikisi ile biyopside granülamotöz keilitin varlığı tanı için yeterlidir. Melkersson Rosenthal sendromu tekrarlayan fasiyal paralizilerin ayırıcı tanısında düşünülmesi gereken bir hastalıktır. Bu yazıda Melkersson Rosenthal sendromu tanısı alan 9 yaşında erkek hasta sunulmuştur.
Melkersson-Rosenthal Syndrome is a neuro-mucocutaneous granulomatous disease. It is characterized by recurrent facial nerve paralysis, orofacial edema and fissured tongue. This syndrome is very rare in childhood, it is more frequently seen in the second and the third decades of life. Classical triad of this syndrome is very rarely seen. MRS usually occurs as monosymptomatic or oligosymptomatic involment. The presence of two or one of the manifestations with granulomatous cheilitis in the biopsy is sufficient to make the diagnosis of Melkersson-Rosenthal Syndrome. In differential diagnosis of recurrent facial paralysis Melkersson-Rosenthal Syndrome must be considered. We present a 9 years old-boy who diagnosed as Melkersson-Rosenthal Syndrome.
Melkersson-Rosenthal Syndrome is a neuro-mucocutaneous granulomatous disease. It is characterized by recurrent facial nerve paralysis, orofacial edema and fissured tongue. This syndrome is very rare in childhood, it is more frequently seen in the second and the third decades of life. Classical triad of this syndrome is very rarely seen. MRS usually occurs as monosymptomatic or oligosymptomatic involment. The presence of two or one of the manifestations with granulomatous cheilitis in the biopsy is sufficient to make the diagnosis of Melkersson-Rosenthal Syndrome. In differential diagnosis of recurrent facial paralysis Melkersson-Rosenthal Syndrome must be considered. We present a 9 years old-boy who diagnosed as Melkersson-Rosenthal Syndrome.
Description
Keywords
Melkersson Rosenthal sendromu, Tekrarlayan fasiyal paralizi, Orofasiyal ödem, Dilde fissür, Melkersson Rosenthal syndrome, Recurrent facial palsy, Orofacial edema, Fissured tongue
Citation
Melek, H. vd. (2007). "Melkersson-Rosenthal sendromu: Bir olgu sunumu". Güncel Pediatri, 5(2), 82-84.