Konjenital tam atriyoventriküler bloklu hastalarımızın özellikleri
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Date
2007
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Uludağ Üniversitesi
Abstract
Amaç: Konjenital atrioventriküler (A-V) tam bloklu çocukların klinik özelliklerinin değerlendirilmesi. Gereç ve Yöntem: UludağÜniversitesi Tıp Fakültesi Pediatrik Kardiyoloji Ünitesinde Ocak 1994 ile Aralık 2005 tarihleri arasında değerlendirilen hastaların hastane kayıtları retrospektif olarak gözden geçirildi ve bu süreler içerisinde konjenital A-V tam blok tanısı almış olan 12 hasta çalışmaya dahil edildi. Bu hastaların tıbbi kayıtları incelendi. Bulgular: Toplam 12 hasta (7 erkek, 5 kız) çalışmaya dahil edildi. Tanı anında hastaların yaşları 1 gün ila 6 yaş arasında değişiyordu (ortalama 16 ay, ortanca 12 ay). Oniki hastanın yedisi bradikardi ve ritim problemi, dördü üfürüm, biri de senkop nedeni ile polikliniğimize gönderilmişti. Bradikardisi olan yedi hastanın dördü intrauterin tanı almıştı. Ekokardiyografi ile bir hastada konjenital olarak düzeltilmiş büyük arterlerin transpozisyonu ve üç hastada ise patent duktus arteriozus saptanmıştı. Toplam altı hastanın annesinde anti-Ro ve anti-La antikoru pozitif bulunmuştu ve bu hastalardan birinde ayrıca neonatal lupusun klinik bulguları da mevcuttu. Tanı anında 12 hastanın ortalama ventrikül ve atriyal hızları sırası ile 54 ± 11 ve 116 ± 24 olarak bulunmuştu. Sekiz hastaya kalp pili takılmıştı. Takip süresi 1 ay ila 11 yaş arasında değişen hastaların son kontrollerindeki yaşları 6 ay ila 13 yaş arasındaydı. Sonuç: Fetal hayatta bradiaritmisi saptanan ve/veya annelerinde anti-Ro/La antikoru pozitif olan fetüslerin tümüne seri ekokardiyografi ile takip yapılması önerilir.
Aim: Evaluation of the clinical features of the children with congenital complete atrioventricular block. Material and Methods: The hospital records of children who had been admitted to the Uludag University Pediatric Cardiology Unit between January 1994 and Nowember 2005 were reviewed retrospectively and a total of 12 patients who were diagnosed as congenital complete A-V block between this period were involved the study. Medical records of these patients were reviewed. Results; A total of 12 patients (7 male and 5 female) were involved the study. The children ranged in age from 1 day to 6 years with a mean age of 16 months and a median age of 12 months at the time of diagnosis. Seven of 12 patients were referred to our unit due to bradycardia and rhythym problem; four of them due to murmur, and the remaining one due to syncope. Intrauterine bradycardia was also detected in four of seven patients with the symptom of bradycardia. On echocardiographic examination, corrected transposition of great arteries was found in one patient, and patent ductus arteriosus in three. Totally, specific anti-Ro and anti-La antibody were detected in the mother of six patients and one of them also had the other symptoms of neonatal lupus syndrome. Mean ventricular and atrial rates of 12 patients, obtained from electrocardiography at the time of diagnosis, were 54 ± 11 and, 116 ± 24 respectively. Pacemaker was implanted in eight patients. The follow up period ranged from 1 months to 11 years. Age at last evaluation ranged from 6 months old to 13 years old. Conclusion: In all fetuses with bradyarrhythmias detected in utero and all fetuses of women with anti-Ro/La antibodies, serial echocardiographic monitoring is strongly advised.
Aim: Evaluation of the clinical features of the children with congenital complete atrioventricular block. Material and Methods: The hospital records of children who had been admitted to the Uludag University Pediatric Cardiology Unit between January 1994 and Nowember 2005 were reviewed retrospectively and a total of 12 patients who were diagnosed as congenital complete A-V block between this period were involved the study. Medical records of these patients were reviewed. Results; A total of 12 patients (7 male and 5 female) were involved the study. The children ranged in age from 1 day to 6 years with a mean age of 16 months and a median age of 12 months at the time of diagnosis. Seven of 12 patients were referred to our unit due to bradycardia and rhythym problem; four of them due to murmur, and the remaining one due to syncope. Intrauterine bradycardia was also detected in four of seven patients with the symptom of bradycardia. On echocardiographic examination, corrected transposition of great arteries was found in one patient, and patent ductus arteriosus in three. Totally, specific anti-Ro and anti-La antibody were detected in the mother of six patients and one of them also had the other symptoms of neonatal lupus syndrome. Mean ventricular and atrial rates of 12 patients, obtained from electrocardiography at the time of diagnosis, were 54 ± 11 and, 116 ± 24 respectively. Pacemaker was implanted in eight patients. The follow up period ranged from 1 months to 11 years. Age at last evaluation ranged from 6 months old to 13 years old. Conclusion: In all fetuses with bradyarrhythmias detected in utero and all fetuses of women with anti-Ro/La antibodies, serial echocardiographic monitoring is strongly advised.
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Keywords
Konjenital, Tam atriyoventriküler blok, Congenital, Complete atrioventricular block
Citation
Semizel, E. vd. (2007). "Konjenital tam atriyoventriküler bloklu hastalarımızın özellikleri". Güncel Pediatri, 5(2), 47-51.